长 QT 并发症状

Overview

长 QT syndrome (LQTS) is an abnormality in the heart's electrical system that may cause very fast and potentially dangerous heart rhythms or arrhythmias called torsade de pointes. These arrhythmias may cause sudden loss of consciousness and in some cases, sudden cardiac death.

"长 QT" refers to the abnormal pattern on an electrocardiogram (ECG), the test that records the electrical activity of the heart. The "QT" interval is the ECG measure of the period when the lower chambers of your heart are triggered to contract and then prepare to contract again. 这些腔室称为心室.

When 长 QT occurs, the interval is longer than usual, triggering a dangerous, abnormal rhythm.

我们治疗长QT综合征的方法

在过去的几十年中, UCSF has helped pioneer breakthroughs in the understanding and treatment of genetic arrhythmias (inherited heart rhythm disorders), 比如长QT综合征. Our team includes electrophysiologists – cardiologists who subspecialize in heart rhythm disorders – as well as experts in general cardiology, 遗传学和遗传咨询. 一起工作, we care for patients and their families by offering evaluations and treatments not available elsewhere in the western United States.

We are committed to helping our patients with long QT syndrome live long, healthy lives. 我们的团队通常可以通过药物治疗来控制这种疾病. 通常更少, patients may require implantable cardioverter defibrillators (ICDs), devices that detect abnormal heartbeats and deliver an electrical shock to reset the heart's normal rhythm. UCSF participated in the clinical trials that led to federal approval of ICDs, 我们提供专家护理, 在ICD插入期间和之后.

Our patients may also have access to experimental therapies being evaluated in clinical trials.

奖 & 识别

是全国顶尖的十大赌博平台排行榜之一
全国最好的心脏病专家之一 & 心脏手术

迹象 & 症状

尽管LQTS的确切频率尚不清楚, 它的患病率可能高达五分之一,000人，可能导致2,000 to 3,000 sudden deaths in children and young adults each year in the United States.

The most common symptom of long QT syndrome (LQTS) is a sudden loss of consciousness or fainting, 叫晕厥. The condition may also cause seizures and in some instances, cardiac arrest and sudden death.

病情的严重程度差别很大. Some people never experience syncope and others may have frequent episodes that could possibly lead to cardiac arrest and sudden death.

It is important to note that 症状 usually occur without warning and are caused by a very fast heart rhythm called torsade de pointes. 晕厥可能发生在体力消耗期间或之后, 情绪兴奋或突然的听觉唤起, 比如闹钟.

诊断

长 QT syndrome (LQTS) is usually diagnosed with an electrocardiogram (ECG), which is a picture of the electrical activity of heartbeats. QT是指在心电图上测量的时间间隔. People with this disorder have a longer QT interval than other people.

心电图并不是一个完美的测试. Some people with the disorder will have normal tests or it might be normal on some days and abnormal on other days.

LQTS is usually inherited, which means it may affect multiple family members. 每一个孩子, 妹妹, or brother of a person with the disorder has a 50 percent chance of inheriting the genetic mutation that causes the condition.

一旦有家庭成员被确诊, 对所有其他家庭成员进行测试是非常重要的. All close relatives should see a cardiologist and have an ECG.

基因检测也可以帮助诊断LQTS. Once genetic testing has identified the genetic mutation causing the condition in a family, other family members can be tested for that same genetic mutation to see if they also inherited it.

If a relative of a person with the disorder has genetic testing and is found not to carry the genetic mutation for the condition, then that relative need not be followed by a cardiologist. 这可以减轻很多压力和担忧.

治疗

通过正确的诊断和治疗, long QT syndrome (LQTS) is a treatable disorder and most deaths are preventable.

Many people with the condition can be treated with medication. A minority of patients need an implantable cardiac defibrillator.

加州大学旧金山分校健康 medical specialists have reviewed this information. It is for educational purposes only and is not intended to replace the advice of your doctor or other health care provider. We encourage you to discuss any questions or concerns you may have with your provider.